Friday 7 August 2015

Nasal Encephalocoele

A nasal encephalocele refers to a the herniation of cranial content in the nasal area. It is one of the causes of craniospinal dysraphism.

Clinical Presentation

Nasal encephaloceles usually present at birth with symptom of obstruction or other complications. It presents as an external swelling on the nose.Swelling is usually soft and skin over the swelling is normal. The swelling increases in size on coughing and straining. Symptoms usually present with obstruction or rhinorhea.

Nasal encephalocele are typically identified in association with a discernible cranial bone defect.

Pathology

Nasal encephalocoeles are anterior encephalocoeles where meningeal herniation occurs through a midline defect in the floor of the anterior cranial fossa.

Radiographic features

MRI
A 18 Y/F  Patient present with birth swelling on nose.


There is well defined lesion in naso-ethmoid region. The lesion appearing hyperintense on T2W & STIR images while hypointense on T1W images. The lesion is communicating with the brain parenchyma through bony defect in fronto-nasal region.
No fat component is seen within the lesion

There is no enhancement of the lesion in post contrast images.

T1W



     
T2W 
 

T1W Plain 
T1W Contrast



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